An Interesting Case of Proteinuria: AL Amyloidosis
نویسندگان
چکیده
Light-chain (AL) amyloidosis is the most common form of systemic and associated with an underlying plasma cell dyscrasia. The disease often difficult to recognise because its broad range manifestations what are vague symptoms. clinical syndromes at presentation include nephrotic-range proteinuria or without renal dysfunction, hepatomegaly, congestive heart failure autonomic sensory neuropathy. Recent diagnostic prognostic advances serum free light-chain assay, cardiac magnetic resonance imaging serologic biomarkers. Treatment strategies that have evolved during past decade prolonging survival preserving organ function in patients this disease. This review outlines approaches diagnosis, assessment severity treatment AL amyloidosis. We describe a case 54--year-old male patient monoclonal gammopathy
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ژورنال
عنوان ژورنال: Vidarbha journal of internal medicine
سال: 2022
ISSN: ['0976-4356']
DOI: https://doi.org/10.25259/vjim_16_2021